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acyl CoA dehydrogenase
Catalyzes first step of beta oxidation of fatty acids.
A number of straight-chain acyl-CoA dehydrogenases of different substrate specificities are present in mammalian tissues.
Laboratory:
- acyl CoA dehydrogenase in fibroblasts
Specific
acyl-CoA dehydrogenase family member 10 (ACAD-10, ACAD10)
acyl-CoA dehydrogenase family member 11 (ACAD-11) (ACAD11)
acyl-CoA dehydrogenase family member 9, mitochondrial; ACAD-9 (ACAD9)
acyl-Coenzyme A dehydrogenase, C-2 to C-3 short chain
acyl-Coenzyme A dehydrogenase, C-4 to C-12 straight chain or medium chain acyl CoA dehydrogenase
acyl-Coenzyme A dehydrogenase, long chain
acyl-Coenzyme A dehydrogenase, short/branched chain
hydroxyacyl-coenzyme A dehydrogenase, mitochondrial; HCDH; medium & short-chain L-3-hydroxyacyl-coenzyme A dehydrogenase; short-chain 3-hydroxyacyl-CoA dehydrogenase (HADH, HAD, HADHSC, SCHAD)
peroxisomal multifunctional enzyme type 2; MFE-2; 17-beta-hydroxysteroid dehydrogenase 4; 17-beta-HSD 4; D-bifunctional protein; DBP; multifunctional protein 2; MPF-2; contains: (3R)-hydroxyacyl-CoA dehydrogenase; enoyl-CoA hydratase 2; 3-alpha,7-alpha,12-alpha-trihydroxy-5-beta-cholest-24-enoyl-CoA hydratase (HSD17B4, EDH17B4)
very long-chain specific acyl-CoA dehydrogenase, mitochondrial; VLCAD (ACADVL, VLCAD)
General
dehydrogenase
flavoprotein
mitochondrial membrane protein
Properties
COMPARTMENT: inner mitochondrial membrane
MOTIF: membrane region
cofactor-binding site
COFACTOR-BOUND: flavin adenine dinucleotide
References
- Textbook of Biochemistry with Clinical Correlations,
3rd ed., TM Devlin (ed), Wiley-Liss, NY 1992 pg 409
- Wikipedia; Note=butyryl-CoA dehydrogenase entry
http://en.wikipedia.org/wiki/butyryl_CoA_dehydrogenase