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acromesomelic chondrodysplasia Grebe type

Genetics: - autosomal recessive - associated with defects in GDF5 Clinical manifestations: - see acromesomelic chondrodysplasia - normal axial skeletons & missing or fused skeletal elements within the hands & feet

General

acromesomelic chondrodysplasia

Database Correlations

OMIM 200700

References

UniProt :accession P43026