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3-hydroxyisovalerylcarnitine
Pathology: - found in serum & urine of patients with 3-methylcrotonyl-CoA carboxylase deficiencyRelated
3-hydroxyisovalerylcarnitine in serum/plasmaGeneral
acylcarnitineProperties
COMPARTMENT: inner mitochondrial membraneReferences
- van Hove JL et al 3-Hydroxyisovalerylcarnitine in 3-methylcrotonyl-CoA carboxylase deficiency J Inherit Metab Dis. 1995;18(5):592-601. PMID: 8598640